Despite Losing Sight, Jockey's Son Cheers on Big Brown

June 5, 2008 -- Big Brown's quest to win the Triple Crown isn't just about horse racing glory. His jockey, Kent Desormeaux, hopes to win Saturday for his young son, who is already deaf and is slowly losing his sight.

Jacob, 9, was born deaf. And doctors have told Desormeaux and his wife, Sonia, that Jacob is likely to lose his vision by early adulthood.

"'He's lost his hearing, but his memory is profound," Kent Desormeaux said. "I'm hopeful that if he's having a bad day, he'll just think about that day that dad won the Triple Crown, and hopefully, that will make him smile."

Even before he was born, Jacob's parents saw evidence their son would have difficulty with his hearing.

"We have a picture, an ultrasound picture of Jacob and he's actually holding onto his ears with both of his hands," Sonia Desormeaux told ABC News. "When he was born, for probably eight to nine months of his life, we would have to literally pry his hands away from his ears and pull them down. And they would go right back up."

After consulting multiple doctors, Jacob was ultimately diagnosed with a rare degenerative disorder, Usher syndrome. Now he has cochlear implants on both his ears. Without them, he'd live in silence.

"When I was born, my ears were broken," Jacob said. "I got a new one when I was 1½."

But in the past few years, his parents noticed another disturbing change when Jacob began losing his eyesight.

"His sight has changed over the last ... two years now," his mother said. "He first started with night blindness, where he just showed up one evening and started screaming for me to help him into the house from the car."

While Jacob knows what is happening to him, his parents said he is just focused on being a kid, with his big brother Joshua, 15.